A transgenic mouse model reproduces human hereditary systemic amyloidosis

Amyloidoses are rare life-threatening diseases caused by protein misfolding of normally soluble proteins. The fatal outcome is predominantly due to renal failure and/or cardiac dysfunction. Because amyloid fibrils formed by all amyloidogenic proteins share structural similarity, amyloidoses may b...

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Bibliographic Details
Main Authors: Chabert, Michèle, Rousset, Xavier, Colombat, Magali, Lacasa, Michel, Kakanakou, Hermine, Bourderioux, Mathilde, Brousset, Pierre, Burlet-Schiltz, Odile, Liepnieks, Juris J., Kluve-Beckerman, Barbara, Lambert, Gilles, Châtelet, François P., Benson, Merrill D., Kalopissis, Athina D.
Format: Online
Language:English
Published: Elsevier 2019
Online Access:Chabert, M., Rousset, X., Colombat, M., Lacasa, M., Kakanakou, H., Bourderioux, M., … Kalopissis, A. D. (2019). A transgenic mouse model reproduces human hereditary systemic amyloidosis. Kidney International. https://doi.org/10.1016/j.kint.2019.03.013
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